Mucinous cystadenocarcinoma of the pancreas during pregnancy

The occurrence of a mucinous cystadenocarcinoma of the pancreas during pregnancy is extremely rare, reported in only twice in the English literature. We describe a 34-year-old patient with this rare condition who was successfully managed by resection of the tumor with distal pancreatectomy and splenectomy. The operation was performed at 15 weeks of gestation, and the patient went on to deliver a healthy infant at 39 weeks. To our knowledge, this is the first report of successful resection of a cystadenocarcinoma of the pancreas during pregnancy. The specimen weighed 2500 g and measured 20 cm across, making it the largest reported mucinous cystadenocarcinoma of the pancreas encountered during pregnancy to date.